Angiographic demonstration of reversible cerebral vasospasm in porphyric encephalopathy.

The porphyrias are rare inherited diseases of heme biosynthesis which can involve the central nervous system. The most frequent clinical manifestations are peripheral neuropathy and mental disturbance (1). Recent studies have proposed vasculopathy as a cause of reversible ischemia (2, 3). We report a case of reversible vasospasm in porphyric encephalopathy demonstrated by both magnetic resonance (MR) angiography and conventional angiography.